Essential thrombocythemia
עודכן לאחרונה 18 Aug 2020
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Essential thrombocythemia is a condition characterised by an increased number of platelets (thrombocythemia). Platelets (thrombocytes) are blood cells involved in blood clotting. While some people with this condition have no symptoms, others develop problems associated with the excess platelets.
תיאור
Essential thrombocythemia is a condition characterised by an increased number of platelets (thrombocythemia). Platelets (thrombocytes) are blood cells involved in blood clotting. While some people with this condition have no symptoms, others develop problems associated with the excess platelets.
Abnormal blood clotting (thrombosis) is common in people with essential thrombocythemia and causes many signs and symptoms of this condition. Clots that block blood flow to the brain can cause strokes or temporary stroke-like episodes known as transient ischemic attacks. Thrombosis in the legs can cause leg pain, swelling, or both. In addition, clots can travel to the lungs (pulmonary embolism), blocking blood flow in the lungs and causing chest pain and difficulty breathing (dyspnea).
Another problem in essential thrombocythemia is abnormal bleeding, which occurs more often in people with a very high number of platelets. Affected people may have nosebleeds, bleeding gums, or bleeding in the gastrointestinal tract. It is thought that bleeding occurs because a specific protein in the blood that helps with clotting is reduced, although why the protein is reduced is unclear.
Other signs and symptoms of essential thrombocythemia include an enlarged spleen (splenomegaly); weakness; headaches; or a sensation in the skin of burning, tingling, or prickling. Some people with essential thrombocythemia have episodes of severe pain, redness, and swelling (erythromelalgia), which commonly occur in the hands and feet.
Inheritance patterns
The source lists the following possible inheritance patterns: Autosomal dominant. More than one pattern can apply in different cases.
Related genes
Other names
Essential thrombocytosis
Primary thrombocythemia
Primary thrombocytosis
Related patient information and medicines
Patient information leaflet
מיאלופיברוזיס
מיאלופיברוזיס מטופל? a condition affecting the bone marrow and its blood cell production. מיאלופיברוזיס מטופל? a serious bone marrow disorder that disrupts your body's normal production of blood cells. Secondary myelofibrosis can be caused by other conditions such as essential thrombocythaemia או polycythaemia rubra vera. Risk factors for myelofibrosis.
Patient information leaflet
האם אני יכול לקחת אמלודיפין וולסרטן יחד?
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האם אני יכול לקחת אמפגליפלוזין ולוסרטן יחד?
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Patient information leaflet
רפואה משלימה ואלטרנטיבית
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בטא-לקטמאזות רחבות טווח
Skin and soft tissue in... So, in fact, practically any area of the body can be infected with E. coli , although some areas are only rarely infected. Other diseases Other diseases associated with E. coli include haemolytic uraemic syndrome (HUS) ו thrombotic thrombocytopenic purpura (TTP). These are rare but serious diseases that occur as a.
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מחלת גבהים
מחלת גבהים can affect people who climb or travel (ascend) to more than 2500 metres (8,000 feet) altitude, particularly if they ascend too quickly. For most people, it causes mild symptoms that improve with rest and with time spent getting used to altitude. However, in some people, it can lead to serious symptoms which can become.
קריאה נוספת והפניות
- Essential thrombocythemia; MedlinePlus, National Library of Medicine.
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