פיברוזיס ריאתי אידיופתי
עודכן לאחרונה 18 Aug 2020
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Idiopathic pulmonary fibrosis is a chronic, progressive lung disease. This condition causes scar tissue (fibrosis) to build up in the lungs, which makes the lungs unable to transport oxygen into the bloodstream effectively. The disease usually affects people between the ages of 50 and 70. Idiopathic pulmonary fibrosis belongs to a group of conditions called interstitial lung diseases (also known as ILD), which describes lung diseases that involve inflammation or scarring in the lung.
תיאור
Idiopathic pulmonary fibrosis is a chronic, progressive lung disease. This condition causes scar tissue (fibrosis) to build up in the lungs, which makes the lungs unable to transport oxygen into the bloodstream effectively. The disease usually affects people between the ages of 50 and 70. Idiopathic pulmonary fibrosis belongs to a group of conditions called interstitial lung diseases (also known as ILD), which describes lung diseases that involve inflammation or scarring in the lung.
The most common signs and symptoms of idiopathic pulmonary fibrosis are shortness of breath and a persistent dry, hacking cough. Many affected individuals also experience a loss of appetite and gradual weight loss. Some people with idiopathic pulmonary fibrosis develop widened and rounded tips of the fingers and toes (clubbing) resulting from a shortage of oxygen. These features are relatively nonspecific; not everyone with these health problems has idiopathic pulmonary fibrosis. Other respiratory diseases, some of which are less serious, can cause similar signs and symptoms.
In people with idiopathic pulmonary fibrosis, scarring of the lungs increases over time until the lungs can no longer provide enough oxygen to the body's organs and tissues. Some people with idiopathic pulmonary fibrosis develop other serious lung conditions, including lung cancer, blood clots in the lungs (pulmonary emboli), pneumonia, or high blood pressure in the blood vessels that supply the lungs (pulmonary hypertension). Most affected individuals survive 3 to 5 years after their diagnosis. However, the course of the disease is highly variable; some affected people become seriously ill within a few months, while others may live with the disease for a decade or longer.
In most cases, idiopathic pulmonary fibrosis occurs in only one person in a family. These cases are described as sporadic. However, a small percentage of people with this disease have at least one other affected family member. When idiopathic pulmonary fibrosis occurs in multiple members of the same family, it is known as familial pulmonary fibrosis.
Inheritance patterns
The source lists the following possible inheritance patterns: Autosomal dominant. More than one pattern can apply in different cases.
Related genes
Other names
Cryptogenic fibrosing alveolitis
Idiopathic fibrosing alveolitis, chronic form
IPF
Usual interstitial pneumonia
Related patient information and medicines
Patient information leaflet
פיברוזיס ריאתי
Pulmonary fibrosis is a serious lung disease where the tiny air sacs of the lungs (the alveoli) and the lung tissue next to the alveoli become damaged and scarred, resulting in lung fibrosis. The main symptom is shortness of breath that gradually gets worse. Pulmonary fibrosis causes The main causes of pulmonary fibrosis are: Unknown (called.
Patient information leaflet
פנאומוטורקס
For example, a pneumothorax may develop as a complication of chronic obstructive pulmonary disease (COPD... Other lung diseases that may be complicated by a pneumothorax include: Pneumonia. Tuberculosis . Sarcoidosis. Cystic fibrosis. Lung cancer. Idiopathic pulmonary fibrosis. אחר causes of pneumothorax An injury to the chest - for example, a.
Patient information leaflet
שיעול כרוני מתמשך במבוגרים
Usually symptoms are being short of breath, tired and having swollen ankles. Occasionally there can be a cough. Pulmonary fibrosis. This is caused by damage and scarring of lung tissue, which causes cough and breathlessness. For more information on these conditions, follow the links where available. All the abo... Sometimes you can be left with an.
Patient information leaflet
מיפוי גליום
A gallium scan uses a radioactive chemical to help create pictures which can show areas of possible infection, injury, inflammation or cancer. It does this by looking for areas where there is rapid cell division within the body. A gallium scan is a type of nuclear medicine, or radionuclide scan. There are differen... Monitor the response to.
Patient information leaflet
כשל נשימתי
Respiratory failure occurs when the breathing system fails to keep adequate blood oxygen levels. There may also be difficulties in removing waste gases, mainly blood carbon dioxide. Why does respiratory... Causes of respiratory failure Common causes of type I respiratory failure Chronic obstructive pulmonary disease (COPD). Pneumonia . Pulmonary.
Patient information leaflet
ספירומטריה
ספירומטריה is a test that can help diagnose various lung conditions, most commonly מחלת ריאות חסימתית כרונית (COPD). Spirometry may also be used to monitor the severity of some other lung conditions... Note: the information below מטופל? a general guide only. ספירומטריה מטופל? כ test of lung function - these tests look at how well your lungs.
קריאה נוספת והפניות
- פיברוזיס ריאתי אידיופתי; MedlinePlus, National Library of Medicine.
- Allen RJ, Guillen-Guio B, Oldham JM, Ma SF, Dressen A, Paynton ML, Kraven LM, Obeidat M, Li X, Ng M, Braybrooke R, Molina-Molina M, Hobbs BD, Putman RK, Sakornsakolpat P, Booth HL, Fahy WA, Hart SP, Hill MR, Hirani N, Hubbard RB, McAnulty RJ, Millar AB, Navaratnam V, Oballa E, Parfrey H, Saini G, Whyte MKB, Zhang Y, Kaminski N, Adegunsoye A, Strek ME, Neighbors M, Sheng XR, Gudmundsson G, Gudnason V, Hatabu H, Lederer DJ, Manichaikul A, Newell JD Jr, O'Connor GT, Ortega VE, Xu H, Fingerlin TE, Bosse Y, Hao K, Joubert P, Nickle DC, Sin DD, Timens W, Furniss D, Morris AP, Zondervan KT, Hall IP, Sayers I, Tobin MD, Maher TM, Cho MH, Hunninghake GM, Schwartz DA, Yaspan BL, Molyneaux PL, Flores C, Noth I, Jenkins RG, Wain LV. Genome-Wide Association Study of Susceptibility to Idiopathic Pulmonary Fibrosis. Am J Respir Crit Care Med. 2020 Mar 1;201(5):564-574. doi: 10.1164/rccm.201905-1017OC.
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- American Thoracic Society. Idiopathic pulmonary fibrosis: diagnosis and treatment. International consensus statement. American Thoracic Society (ATS), and the European Respiratory Society (ERS). Am J Respir Crit Care Med. 2000 Feb;161(2 Pt 1):646-64. doi: 10.1164/ajrccm.161.2.ats3-00. No abstract available.
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